Ela e caracterizada pela ausencia congenita do terco superior da vagina, utero e trompas. Rokitansky mayer kuster hauser syndrome with multiple leimyomas. E mais comumente associada com malformacoes renais. Mrkh may be isolated type i but it is more frequently associated. Sindrome di mayer rokitansky kuster hauser animrkhs. Role of imaging to identify and evaluate the uncommon variation in development of the female genital tract. Request pdf rokitansky kustner hauser syndrome a case report rokitansky kuster hauser syndrome, also called uterovaginal aplasia, was first described at the beginning of. This condition causes the vagina and uterus to be underdeveloped or absent, although external genitalia are normal. Mayer rokitansky kuster hauser syndrome diagnosed by magnetic resonance imaging. Affected women usually do not have menstrual periods due to the absent uterus. Resumo mayer rokitansky kuster hauser sindrome acomete um em cada 4.